Adult-type fibrosarcoma is a rare and highly aggressive subtype of soft tissue sarcomas. Due to the existence of other spindle-cell shaped sarcomas, its diagnosis is always one of exclusion. The likelihood of misdiagnoses between similar tumour entities is high, and often leads to inappropriate tumour treatment. We summarize here the main features of fibrosarcoma.
Adult Soft Tissue Sarcoma Treatment (PDQ®)–Patient Version - National Cancer Institute
Fibrosarcoma is a rare type of cancer that affects cells known as fibroblasts. Fibroblasts are responsible for creating the fibrous tissue found throughout the body. Tendons, which connect muscles to bones, are made up of fibrous tissue. When fibrosarcoma strikes, the body's fibroblasts lose control and multiply excessively.
Adult Soft Tissue Sarcoma Treatment (PDQ®)–Patient Version
The soft tissues of the body include the muscles, tendons bands of fiber that connect muscles to bones , fat, blood vessels , lymph vessels , nerves , and tissues around joints. Adult soft tissue sarcomas can form almost anywhere in the body, but are most common in the head, neck, arms, legs, trunk , abdomen , and retroperitoneum. Enlarge Soft tissue sarcoma forms in soft tissues of the body, including muscle, tendons, fat, blood vessels, lymph vessels, nerves, and tissue around joints. There are many types of soft tissue sarcoma.
Fibrosarcoma fibroblastic sarcoma is a malignant mesenchymal tumour derived from fibrous connective tissue and characterized by the presence of immature proliferating fibroblasts or undifferentiated anaplastic spindle cells in a storiform pattern. It is usually found in males aged 30 to It also involves periosteum and overlying muscle.